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Pathways of ammonia detoxification to GLN in muscles linked to Improved consumption of the BCAA and α-KG (cataplerosis) and recommended outcomes of BCAA and phenylbutyrate in topics with liver cirrhosis or UCD. Good outcome of BCAA on ammonia detoxification to GLN could be blunted by GLN degradation to ammonia in enterocytes and kidneys. Phenylbut